Colorectal Conundrum: October 9, 2023

Ron Reeder • Oct 09, 2023

For Quiz & Answers to the October 2nd Conundrum - see the blog post here.


Colorectal Conundrum for October 9th:

A patient with a cloaca undergoes cystoscopy and a urethra is identified and a rectal fistula but no orifice for a vagina is seen. The cloacagram is shown as is the view done by a diagnostic laparoscopy. What is your interpretation of this patient’s cloacal anatomy and of her intraabdominal Mullerian anatomy?

Answer for October 9th:

This rare cloaca has a common channel that goes directly into the bladder. There is only a rectal fistula and no distal vagina at all on scope. Laparoscopy shows Mullerian remnants. It is impossible to know at this point what will become of those structures upon hormonal stimulation at puberty. So the ideal treatment is to perform that rectoplasty via a PSARP approach and leave the common channel alone and disconnect the rectal fistula from the good lumen rectum and close it over with absorbable suture. At puberty, a pelvic ultrasound after thelarche would reveal if there is growth of the vagina, and if so, that structure could be pulled through the old rectal fistula removed. If no Mullerian structures develop the rectal fistula could be dilated at a later age when the patient is able to do that.

How would you handle this case?

By Ron Reeder 29 Jan, 2024
Colorectal Conundrum for January 29: A male with a rectoperineal fistula undergoes a PSARP with mobilization of the rectum, both anterior and posterior rectal walls. In the days following surgery he starts to drain urine around the anoplasty consistent with a urethral injury. He is also voiding via the penis. A cystogram is shown below. How would you manage this situation? Answer: This patient has suffered from a urethral injury, and urine is draining out the posterior urethra into the perineum around the anoplasty. The key first step is to divert the urine with a suprapubic tube. A colostomy is not necessarily needed. The fistula might heal with diversion. If after a month or so a cystogram shows the persistence of the fistula, then a redo is needed with re-mobilization of the rectum, fully lifting the anterior rectal wall off of the urinary tract, and repair the urethra, with coverage of the posterior urethra with an ischiorectal fat pad. Then a voiding trial a month later with ultimate removal of the SP tube.
By Ron Reeder 22 Jan, 2024
Colorectal Conundrum for January 22nd: In the previous week’s case, of an imperforate hymen, the MRI showed dilation all the way down to the perineum. Management involved a perineal – introital – incision to drain the fluid. If that were not the case and you had a dilated vagina but the distal extent was far away from the introital area, how might you handle that hydrocolpos? Answer: If this were a case of hydrolpos with normal anus and normal urethra, and the vagina cannot be drained by the introitus like an imperforate hymen, then drainage needs to be from above. IR or laparoscopy is an ideal approach to get a drain in the dilated structure (remember this could be bilateral, so both sides may need to be drained. Drainage is to relieve distension and most concerning its potential cause of distal ureteral obstruction causing hydronephrosis. Once the material hormones have dissipated the hydrocolpos will resolve and can be dealt with later in life via a laparoscopic distal vaginal pull-through, after the onset of puberty. In such a patient, I would follow closely with ultrasound 6 months after thelarche (breast budding).
By Ron Reeder 16 Jan, 2024
Colorectal Conundrum for January 16: A newborn female is noted to have abdominal distension. On exam the uretha and anus are normal, and there appears to be a bulge in the hymen. The has an MRI with the image shown below. What would be your treatment plan? What are the variations in such a case and how would you manage each? Answer: This could be a case of imperforate hymen, but the MRI is key – how high up is the obstruction? How large is the hydrocolpos? In this case, it appears that a perineal incision might all that is needed as the dilation extends all the way down to the perineum. That is the most common scenario. An incision at the level of the hymen should drain out the fluid and no further intervention should be needed. Of course a careful exam needs to check to be certain you see a urethra – sometimes such a bulge could be a paraurethral cyst. For the next week’s question – what would you do if the perineal approach was inadequate – i.e. could not reach the dilated lumen.
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